Síndrome del incisivo central único de la línea media del maxilar y fusión de incisivos centrales permanentes mandibulares: Reporte de un caso clínico

Abstract

The solitary median maxillary central incisor syndrome is not a very frequent anomaly, and is characterized mainly by structural malformations of the craniofacial area. The most significant clinical characteristic is in the oral cavity, with the presence of a unique incisor enveloped in the half line of the maxillary in both dentitions (primary and permanent). This report describes a 6 year old girl with a unique incisor enveloped in the half line of the maxillary and other abnormalities were detected: absence of the labial frenulum, fusion of central teeth and oval palate. The presence of the unique incisor will always be associated to other anomalies, such as: deficit of growth hormone and Triple X syndrome; besides being considered a holoprosencephaly predictor.